ISSN : 1301-5680
e-ISSN : 2149-8156
TURKISH JOURNAL OF
THORACIC AND
CARDIOVASCULAR SURGERY
Turkish Journal of Thoracic and Cardiovascular Surgery     
Incidence and treatment of pulmonary vein stenosis after repair of total anomalous pulmonary venous connection
Ersin Erek1, Dilek Suzan1, Selim Aydın1, Ramal Hesenov1, Bahar Temur1, Barış Kırat2, Okan Yıldız3, İbrahim Halil Demir4, Ender Ödemiş4
1Department of Pediatric Cardiac Surgery, Acibadem Mehmet Ali Aydinlar University School of Medicine, Istanbul, Turkey
2Department of Anesthesiology and Reanimation, Acibadem Atakent Hospital, Istanbul, Turkey
3Department of Pediatric Cardiac Surgery, Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Training and Research Hospital, Istanbul, Turkey
4Department of Pediatric Cardiology, Acibadem Atakent Hospital, Istanbul, Turkey
DOI : 10.5606/tgkdc.dergisi.2019.17303
Background: In this study, we aimed to investigate the incidence and treatment of pulmonary vein stenosis after repair of total anomalous pulmonary venous connection.

Methods: Between December 2010 and December 2016, a total of 40 patients (25 males, 15 females; mean age 45±41 days; range, 2 days to 6 months) who underwent total anomalous pulmonary venous connection repair were retrospectively analyzed.

Results: Eighteen (45%) of the patients were supracardiac, seven (17.5%) were cardiac, eight (20%) were infracardiac, and seven (17.5%) were mixed-type anomaly. Twelve patients (30%) had obstruction of the pulmonary venous pathways. Hospital mortality was seen in three patients (7.5%). All of non-survivors received emergent surgery and the causes of death were sepsis and multiple organ failure. A total of 23 complications were seen in 20 patients (50%) mainly delayed sternal closure (n=11; 27.5%) and prolonged mechanical ventilation (n=6; 15%). The mean follow-up was 12.2±9.6 (range, 1 to 36) months in all patients, except one. Pulmonary vein stenosis developed in three patients (8.3%) after repair. All of them underwent sutureless repair.

Conclusion: Total anomalous pulmonary venous connection can be repaired with low mortality and morbidity rates and favorable mid-term outcomes. Close follow-up is necessary due to the risk of development of pulmonary vein stenosis. Sutureless repair may provide relief in such cases.

Keywords : Congenital heart surgery, infant, pulmonary vein stenosis, total anomalous pulmonary venous connection
Viewed : 240
Downloaded : 106